This thesis will describe the clinical phenotypes, with emphasis on electrophysiology, in patients with different hereditary eye diseases and to further evaluate and modify the mfVEP technique for clinical use. Bothnia Dystrophy is a tapetoretinal disorder with a mutation in the RLBP1 gene. Early in the disease the fundus may have a normal appearance. The full-field ERG demonstrates an absence of

1. The objective of the present study was to examine the role of the endothelial selectins (i.e. P- and E-selectin) in leukocyte-endothelium interactions in colonic venules by use of intravital microscopy. 2. Balb/c mice were exposed to dextran sodium sulphate (DSS) in the drinking water for 5 days or treated intraperitoneally (i.p.) with tumour necrosis factor-alpha (TNF-alpha) for 3 h. 3. In DSS

Alport syndrome (AS) is a type IV collagen hereditary disease characterized by progressive hematuric nephritis, hearing loss, and ocular changes. Mutations in the COL4A5 collagen gene are responsible for the more common X-linked dominant form of the disease characterized by much less severe disease in girls and women. A "European Community Alport Syndrome Concerted Action" (ECASCA) group was estab

Cultural and moral dimensions of waste.

This volume provides a compilation of recent contributions on feedback and robust control, modeling, estimation and filtering. They were presented on the occasion of the sixtieth birthday of Anders Lindquist, who has delivered fundamental contributions to the fields of systems, signals and control for more than three decades. His contributions include seminal work on the role of splitting subspace

A new approach to calculating the parameters of resonant states is proposed, which also makes it possible to determine the probabilities of the resonant scattering and capture probabilities at the resonant state. This approach is based on the application of the method of configuration interaction, which was proposed for the first time by Fano for an analysis of field ionization of the helium atom.

A study was made of the damped oscillations in fibre length that are observed when isolated muscle fibres from the frog are released during the plateau of an isometric tetanus to shorten against a constant load (force clamp recording) near the isometric level (temperature, 1.0-11.0 C; initial sarcomere length, 2.25 m). 2. The oscillatory length changes of the whole fibre were associated with simil

Changes in the composition of carrot cell wall proteins were investigated, associating metabolic changes during long-term storage with changes in mechanical properties. Harvested carrots accumulate an antifreezing protein in their cell walls reaching a maximum level after 12 weeks of storage at 0°C, followed by a gradual decrease. During the same period of time, there is a decrease in the slicing

Sub-picosecond laser pulse driven localization of electronic excitation energy is suggested for a biological chromophore complex. Based on an exciton model of the photosynthetic core antenna PSI of Synechococcus elongatus the shape of the respective laser pulse is calculated using optimal control theory combined with a density matrix theory accounting for energy relaxation and dephasing caused by

Lifetimes of high spin states in the three A = 89 isobars Nb-89, (89)MO and (TC)-T-89 have been measured via the Recoil Distance Doppler Shift technique and the fusion evaporation reactions Ni-58(Cl-35, xnypz alpha) at 120 MeV beam energy. Reduced transition probabilities for about 50 gamma transitions were extracted. The experimental branching ratios in Mo-89 and reduced transition probabilities